Von Willebrand Factor Top Journals

Von Willebrand Factor Top Journals

Citations are important for a journal to get impact factor. Impact factor is a measure reflecting the average number of citations to recent articles published in the journal. The impact of the journal is influenced by impact factor, the journals with high impact factor are considered more important than those with lower ones. Impact factor plays a major role for the particular journal. Journal with higher impact factor is considered to be more important than other ones. Impact factor can be calculated as average number of citation divided by recent cited articles published in 2 years. Most commonly inherited bleeding disorder, first described in Aland Islands by Erik von Willebrand. It occurs as a result of decrease in plasma levels or defect in von Will brand factor which is a large multimeric glycoprotein. Monomers of this glycoprotein undergo N-glycosylation to form dimers which get arranged to give multimers. Binding with plasma proteins (especially factor VIII) is the main function of von Willebrand factor. The disease is of two forms: Inherited and acquired forms. Inherited forms are of three major types. They are type 1, type 2, and type 3; in which type 2 is sub-divided into 2A, 2B, 2M, 2N. Type 1 is more prevalent than all other types. Mucocutaneous bleeding is mild in type 1 whereas it is mild to moderate in types 2A, 2B, and 2M. Type 2N has similar symptoms of haemophilia. The pathophysiology of each type depends on the qualitative or quantitative defects in von Willebrand factor. The diagnosis is based on von Willebrand factor antigen, von Will brand factor activity assay, FVIII coagulant activity and some other additional tests. Results should be analyzed within the context of blood group. von Willebrand factor multimer analysis is essential for typing and sub typing the disease. The management of the disease involves replacement therapy, non-replacement therapy and other therapies that include antifibrinolytics and topical agents. As already mentioned, the specific domains present in it are responsible for its functions. The main function is to bind with plasma proteins, especially factor VIII and coagulate blood[7]. Factor VIII in its inactive state binds to VWF in the circulation. If it is unbound, it rapidly degrades. When VWF is exposed in endothelium during an injury to blood vessel, it binds to collagen. When coagulation is stimulated, the platelet receptors get activated. VWF binds to these activated receptors. VWF binds to platelet glycoprotein Ib (GPIb) receptor when it forms a complex with glycoprotein IX (GPIX) and glycoprotein V (GPV). This occurs when there is a rapid flow in narrow blood vessels. Studies show that VWF uncoils and decelerate platelets under these conditions.

 


Last Updated on: Nov 30, 2024

Global Scientific Words in Neuroscience & Psychology